Pachydermoperiostosis with myelofibrosis and empty sella.
نویسندگان
چکیده
A case of pachydermoperiostosis presented to us in rheumatology clinic with complaints of pain and swelling in knee joints unresponsive to treatment, characteristic facial features, grade four clubbing of nails and broadening of distal parts of extremities. He also complained of fatiguability which was due to anemia. The natural history of the disease was reviewed and investigated.
منابع مشابه
Prevalence of empty sella syndrome
Background: The empty sella syndrome (ESS) is a neurological or pathologic finding in which sella turcica is devoid of pituitary tissue and the subarachnoid space extends into sella turcica, which is either primary or secondary as well as partial and complete. The widespread use of CT scans and MRIs today has made the ESS a common finding in imaging. The aim of this study was to evaluate the pr...
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Empty sella is a radiological-anatomical entity characterised by a sella turcica filled partially or completely with cerebrospinal fluid, leading to varying degrees of pituitary flattening. Literature reports a 5% 20% incidence of empty sella in unselected autopsies leading many to argue that it is an extreme normal variant. Endocrine dysfunction varies from 8% 25% with primary empty sella and ...
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A case of 'low tension glaucoma' with primary empty sella is reported. The visual field defect and optic disc change were characteristic of glaucoma. The intraocular pressure was within normal limits. X-ray examination and the metrizamide-CF procedures revealed a primary empty sella. The coexistence of 'low tension glaucoma' and empty sella is discussed.
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ورودعنوان ژورنال:
- The Journal of the Association of Physicians of India
دوره 58 شماره
صفحات -
تاریخ انتشار 2010